ABSTRACT
Syringocystadenoma papilliferum (SCAP) is an uncommon benign hamartomatous adnexal tumor. It arises from pluripotential cells and histology exhibits apocrine or eccrine differentiation even if it is still classified under tumors with apocrine gland differentiation. The lesions are usually seen at birth or in childhood. The preferential location is the scalp, followed by the head and neck, often with coexistent nevus sebaceous. There are three recognized clinical forms: plaque, solitary nodular and linear. Most of the lesions are sporadic cases and are diagnosed on histopathology. Rarely, malignant transformation has been documented.
