ABSTRACT

This disorder is noted at birth or shortly thereafter. It occurs in 4.4% of African-American infants, whereas only 0.2% of Caucasian-American infants are affected.1 Typically, pustules are noted, especially on the neck, face, and trunk. Pustules may also be present on the palms and soles. Hyperpigmented macules may occur following a pustular lesion or can be noted at birth or without a history of a preceding pustule (Figure 3.1). The pustules are easily ruptured and are sterile when cultured, and the contents contain neutrophils when examined microscopically.