ABSTRACT
Introduction Truncus arteriosus (TA) is a comparatively rare (2-3% of all defects) congenital lesion
consisting of a single great vessel arising from the heart. A single semilunar valve is present. This single great vessel (truncus) gives rise to the coronary arteries, aorta and pulmonary arteries (PAs). Almost invariably a ventricular septal defect (VSD) is present. One-third of patients with TA have DiGeorge syndrome characterized by thymic aplasia/hypoplasia, hypoparathyroidism, hypocalcemia, dysmorphism and chromosome deletion (22p11).
