ABSTRACT
Uterine sarcomas are rare tumours that account for approximately 1% of female genital tract malignancies and 2-8% of uterine cancers. Despite representing a small proportion of uterine cancers, sarcomas account for a disproportionately high fraction of deaths. Data from a Norwegian cancer registry found that uterine sarcomas are responsible for 26% of mortalities from uterine cancers. The worldwide annual incidence of uterine sarcoma is between 0.5 and 3.3 cases per 100,000 women. According to SEER analysis of 2677 cases of uterine sarcoma in US, the overall age-adjusted incidence for black women was twice that of whites and more than twice that of women of other races. Overall, 45-54% of patients presented with stage 1 disease while overall 5-year survival was 40-50%.
