ABSTRACT
LAM should be considered in any woman with an unexplained pneumothorax, particularly in the pregnant or young, nonsmoking patient. Chylothorax should also suggest the diagnosis in any female of childbearing age without a readily apparent alternative etiology. LAM can also present less frequently with hemoptysis (especially with exertion), chyloptysis, chyluria, chylous ascites, or chylopericardium. Rarely, abdominal complaints may predominate. Extensive lymphadenopathy may prompt an evaluation for malignancy, such as ovarian cancer or lymphoma.
