ABSTRACT
Tumors of the ear 570 Epithelial tumors 570
Aggressive papillary middle-ear tumor 570 Ceruminoma 570 Middle-ear adenoma 571
Miscellaneous tumors 571 Inflammatory masses 571 Other rare tumors 571
Neuroendocrine tumors 571 Glomus jugulare 571
Tumors of the nasopharynx 572 Epithelial tumors 572
Inverted papilloma of nose 572 Mucosal gland adenomas 572 Olfactory neuroblastoma 573
Mesenchymal tumors 574 Angiofibroma, juvenile nasopharyngeal 574
Miscellaneous tumors 575 Mucous membrane plasmacytosis of the upper
aerodigestive tract 575 Other tumors 575
Tumors of the oral cavity 576 Epithelial tumors, benign 576
Microcystic papillary adenomas 576 Squamous papilloma 576
Epithelial tumors, malignant 576 Squamous carcinoma 576
Mesenchymal tumors 577 Ectomesenchymal chondromyxoid tumor of the tongue 577
Miscellaneous tumors 578 Giant cell granuloma (epulis) 578 Salivary gland tumors 579 Wegener’s granulomatosis 579
Tumors of the jaw 579 Odontogenic cysts and cystic lesions 579
Dentigerous (follicular) cyst 580 Gingival cysts 580 Inflammatory odontogenic cysts 580
Lateral periodontal, botryoid, and glandular cyst 581 Odontogenic keratocyst (primordial cyst) 582
Odontogenic tumors 583 Adenomatoid odontogenic tumor 583 Ameloblastic fibroma and related lesions 584 Ameloblastoma 585 Calcifying epithelial odontogenic tumor 587 Cementoma (cementoblastoma, gigantiform cementoma,
periapical cemental dysplasia and cementifying fibroma) 587 Clear cell odontogenic tumor 588 Malignant odontogenic tumors: odontogenic carcinomas
and sarcomas 589 Odontogenic fibroma 590 Odontogenic myxoma 590 Odontomas 591 Squamous odontogenic tumor 591
Tumors of the salivary glands 592 Epithelial tumors, benign 593
Basal, membranous, canalicular, trabecular, sebaceous and tubular monomorphic adenomas 593
Basal cell adenoma 593 Membranous adenomas (dermal anlage tumor) 594 Hybrid basal cell adenoma 594 Canalicular adenoma 594 Sebaceous adenoma 594 Tubular adenoma 594
Myoepithelioma 594 Oncocytoma 596 Pleomorphic salivary adenoma 597 Warthin’s tumor 599
Epithelial tumors, malignant 600 Acinic cell carcinoma 600 Adenoid cystic carcinoma 601 Basaloid carcinoma 602 Clear cell carcinoma 603 Epithelial-myoepithelial carcinoma 603 Mucoepidermoid carcinoma 603 Polymorphous low-grade adenocarcinoma/terminal
duct carcinoma 605 Salivary duct carcinoma 605
Miscellaneous tumors 607 Benign lymphoepithelial lesion 607 Inverted ductal papilloma of minor salivary glands 609 Necrotizing sialometaplasia 609 Salivary gland choristoma 609 Sialadenoma papilliferum 609
Aggressive papillary middle-ear tumor is a distinct entity with a propensity for local and intracranial invasion and bone destruction, but the lesions do not metastasize. The tumor affects young and middle-aged adults (aged 26-55 years), and is usually asymptomatic, though it may present with hearing loss, tinnitus, facial weakness, otitis or vertigo. There is an association with von Hippel-Lindau disease.
