ABSTRACT
Congenital lung abnormalities are uncommon and diverse in
their presentations. However, all those who care for infants
and children must have an appreciation for the diagnosis and
treatment of these anomalies because the potential conse-
quences can be life threatening. In order to understand the
pathophysiology of these malformations, one must have a
basic understanding of the embryology of lung development,
as well as lung anatomy and respiratory physiology, which are
presented below. Classical lesions including lobar emphyse-
ma, congenital pulmonary airway malformation (CPAM),
pulmonary sequestration, and congenital lung cysts will be
discussed below, along with a number of the less common
anomalies.
