ABSTRACT
Phenylalanine hydroxylase (phenylalanine
4-monooxygenase; E.C. 1.14.16.1)
l-Phenylalanine 0l-tyrosine
This vertebrate enzyme degrades dietary
phenylalanine in excess of requirements for
protein and hormone formation. In a group of
closely associated inherited diseases in man (e.g.
phenylketonuria, hyperphenylalaninaemia) that
