ABSTRACT
Hypertrophic cardiomyopathy, a primary myocardial disorder of sacromeric proteins with an autosomal dominant pattern of inheritance is characterized by asymmetric hypertrophy of the septum with or without dynamic obstruction of the outflow tract (1,2). The prevalence in the general population is estimated as 1:500 and it is the most common monogenic cardiac disorder. Annual mortality in an unselected population is reported to be about 1% to 2%, and sudden death is the most common cause. Sudden death is assumed to be due to idiopathic ventricular arrhythmias, but hemodynamic factors and myocardial ischemia may be involved as well.
