ABSTRACT

The capillary hemangioblastoma is defined by the World Health Organization as a Grade 1 neoplasm of uncertain histogenesis composed of stromal cells and abundant capillaries (Böhling et al., 2000). Initial descriptions by Lindau (1926) and Cushing and Bailey (1928) emphasized the typical cerebellar location (‘Lindau’s tumor’) and frequent cystic character (Sargent and Greenfield, 1929). Involvement of other sites such as the brainstem and spinal cord was subsequently recognized, especially in patients with Von Hippel-Lindau (VHL) disease.