ABSTRACT
Inherited corneal disorders were first reported in 1890 by Groenouw, who described two patients with bilateral corneal opacifications in a nodular form (1). About half a century later, Bu¨cklers stated that at least three different types of such corneal disorders exist and stressed their familial nature and their different modes of inheritance (2). In the next 50 years, thousands of articles were published on the subject of inherited corneal diseases, resulting in frequent confusion in the clinical understanding of these diseases. Most of these publications described the clinical appearance of various corneal dystrophies.
