ABSTRACT

I. Introduction ...........................................................................................................................351 II. Aorta and Large Arteries ......................................................................................................351 III. Microvasculature ...................................................................................................................352 IV. Veins ......................................................................................................................................353 V. Diagnosis ...............................................................................................................................353 VI. Differential Diagnosis ...........................................................................................................354 VII. Prognosis ...............................................................................................................................355 VIII. Treatment...............................................................................................................................355 References ......................................................................................................................................357

Relapsing polychondritis (RP) is a rare disorder characterized by recurrent inflammatory episodes affecting nonarticular cartilaginous structures, mainly the external ear(s), nose, larynx, and tracheobronchial tree, sometimes leading to cartilage destruction.