ABSTRACT
Portopulmonary hypertension (POPH) is a well-recognized type of pulmonary artery hypertension (group 1 in the Dana Point 2008 classification) that occurs in association with portal hypertension (1,2). First recognized by Mantz and Craige in 1951 (3), enhanced recognition and renewed importance of POPH has evolved in the era of liver transplantation (LT) due to the unanticipated complications (increased mortality) when transplantation has been attempted in the setting of untreated, moderate to severe pulmonary artery hypertension (4).
