ABSTRACT

The epileptic spasms associated with this disorder typically occur as brief, symmetrical contractions of the musculature of the neck, trunk, and extremities. The intensity and pattern of distribution of the spasms is highly variable, and three main types of motor spasms may occur: exor, extensor, and mixed exor-extensor. Less commonly, asymmetrical spasms may be seen, and periods of behavioral arrest may occur following a motor spasm. The ictal events may occur in isolation, but most frequently occur in clusters. The spasms may occur throughout the day and night, but rarely occur during sleep. Instead, they frequently occur immediately upon arousal from sleep.