ABSTRACT

Severe radial deviation of the wrist is characteristically seen in children with radial club hand and severe ulnar deviation is seen in children with ulnar club hand. The primary cause of varus deformity of the wrist is disproportionate shortening of the ulna as a result of growth arrest due to an osteochondroma situated on the distal ulna. While the wrist deformity may be the most obvious, the abnormalities of the entire limb including the forearm, elbow and wrist need to be addressed if the appearance and function of the limb are to improve. Madelung deformity is a rare entity caused by an inherited condition called dyschondrosteosis which is transmitted by an autosomal dominant gene. The deformity at the wrist is due to an abnormality of growth of the ulnar half of the distal radial physis brought about by a soft tissue tether. The primary cause of varus deformity at the wrist is the short ulna.