ABSTRACT
Background The family of neuroendocrine tumors Neuroendocrine tumors (NETs) are relatively rare disease entities derived from the diffuse endocrine system, and found anywhere in the body. They often present as a bizarre diagnostic puzzle.1 The fact that these malignancies arise from hormonally active cells explains the wide variety of symptoms encountered in NET patients of various origin. The different manifestations are related to the release of hormones or other biologically active substances produced in excessive amounts, such as insulin, gastrin, vasoactive intestinal peptide (VIP), glucagon, or serotonin.2
