ABSTRACT

References 204

Achalasia of the esophagus is a neuromuscular (1-7) disorder in which esophageal

dilation and hypertrophy occur without organic stenosis. It is characterized by an increased

resting pressure of the lower esophageal sphincter (LES), failure of complete relaxation of

the LES in response to swallowing, and absence of normal esophageal peristalsis. The

incidence of achalasia is one in 10,000 people (8,9). It is a relatively uncommon

problem in children, with those under 15 years of age comprising ,5% of the symptomatic cases (10-12). Presenting symptoms include regurgitation of food, dysphagia,

and failure to thrive. Respiratory difficulties may also be present and are often the

result of chronic aspiration.