Results

Adjuvant treatment Because of the usual site of these tumors, adjuvant radiation is difficult to deliver. Where this can be delivered safely, it should be applied.

Results In a review from the Armed Forces Institute of Pathology, 38 cases of inflammatory fibrosarcoma were described, with a median age of 8.5 years (2 months to 74 years), the majority

with symptoms of pain, anemia, fever or gastrointestinal obstruction.39 The majority occurred in the mesentery or retroperitoneum, with only rarely identified tumors elsewhere. Approximately one-third of the patients had a local recurrence, and 10% had histologically proven distant metastases. Characteristically, a patient who first presented with an inflammatory pseudo-tumor and then developed severe pain and fever was shown to have an inflammatory fibrosarcoma still containing residual elements of the more benign-appearing low-grade pseudo-tumor (Figure 7.25).