ABSTRACT
The patient is a 22-year-old man who developed normally until his first seizure at 3 years of age. Initially, his seizures were characterized by myoclonic jerks of the upper limbs. The seizures increased in frequency until they occurred many times a day during infancy. Over time the seizures changed and began to include impaired consciousness, pallor, abdominal pain, the expression of fear, mydriasis, motor automatisms and complex visual hallucinations. They often had a long duration and occurred in clusters. Other seizures were characterized by a staring gaze, diffuse hypertonia and clonic jerks of the upper limbs.
