ABSTRACT
The most severe and, in its presentation, most dramatic congenital anomaly of the bladder is ectopia vesicae. In this condition, there is failure of development of the lower abdominal wall, adjacent bony pelvis and external genitalia, such as to lead to deficiencies in various muscles and bones and also to leave the bladder as an open disc on the surface of the lower abdominal wall. The condition is also associated with epispadias, an abnormality of the external genitalia. The management of ectopia vesicae is solely within the remit of a paediatric urologist.
