ABSTRACT
Unfortunately, the prognosis for severe scoliosis is often poor once serious complications such as respiratory failure have appeared. Long term oxygen therapy may prolong life.
Figure 14.6: cystic fibrosis – hyperinflated lungs with marked upper zone interstitial shadowing and basal tramline shadows due to bronchiectasis
Cystic fibrosis is a rare genetically linked disease which occurs in one in 2,000 live births. It affects the body’s mucus secreting glands. The clinical features of the disease relate mainly to the increased viscosity of this mucus. There is defective chloride transport across the respiratory and sweat duct epithelial cells with increased sodium transport.
