ABSTRACT
Congenital masses of the nasal midline are very rare, occurring in 1 in every 20,000-40,000 newborns. Although benign, these masses may cause large facial deformities such as hypertelorism, cerebrospinal fluid (CSF) fistulas, cerebral herniation, visual alterations, meningitis, and cerebral abscess. At an early stage of development during the third and fourth weeks, there is a protrusion of the forebrain and dura through the foramen cecum into the prenasal space, which is limited by frontal and nasal bones on the anterior aspect and posteriorly by a cartilaginous capsule. Gliomas of the nose are rare, always benign heterotopias; they should not to be considered as tumors. The intranasal type is located high in the nasal fossa. The septum may be displaced, and the nasal passage may be obstructed. Preoperative imaging is essential for an appropriate surgical approach by delineating the exact site and extension of the tumor.
