ABSTRACT

The term porokeratosis encompasses a variety of clonal disorders of keratinization characterized by marginate scaling lesions. Five clinical variants of porokeratosis are recognized: classic porokeratosis of Mibelli, disseminated superficial actinic porokeratosis (DSAP), porokeratosis palmaris et plantaris disseminata, linear porokeratosis, and punctate porokeratosis. 13