ABSTRACT
Ongenital pulmonary adenomatoid malformation (CPAM) is characterised by an adenomatoid increase of terminal respiratory bronchioles that form cysts of various sizes. The most common site of involvement for congenital lobar emphysema is the left upper lobe, followed by the right middle lobe, right upper lobe, lower lobes, and multiple sites for the remainder. CPAMs usually arise from one lobe of the lung, with the lower lobes being the most common site; bilateral lung involvement is rare. The most widely accepted embryologic theory is that a supernumerary lung bud arises caudal to the normal lung bud and continues to migrate caudally with the oesophagus. If supernumerary lung development occurs subsequent to pleura formation, the bud will grow separately and acquire its own pleural covering, forming an extralobar sequestration. Typically, the lung tissue in Bronchopulmonary sequestrations receives all or most of its blood supply from an anomalous systemic artery, with the origin of this artery being variable.
