ABSTRACT

The connective tissue diseases (CTDs) by definition involve multiple organs of

the body. Similarly, these CTD may involve multiple anatomic areas of the lungs

and extrapulmonary thorax, which can influence the course of disease. Although

interstitial lung disease (ILD) is the most common manifestation of most of the

CTD, a separate chapter is focused on the pathology, treatment, and clinical

outcome of the many ILD presentations. Dr. Nunes and colleagues reviewed the

pleural and non-ILD pulmonary manifestations of the CTD in chapter 19.