ABSTRACT
A1 C Congenital lobar emphysema is a congenital cystic lung lesion in which the fundamental abnormality consists of an abnormal bronchus that allows passage of air on inspiration but only limited expulsion of air on expiration leading to lobar overexpansion. These lesions do not always cause symptoms. In severe cases, prenatal hydrops or postnatal fatal respiratory distress can occur. The most common site of involvement for congenital lobar emphysema is the left upper lobe (40%–50%), followed by the right middle lobe (30%–40%), right upper lobe (20%), lower lobes (1%) and multiple sites for the remainder.
