chapter  77
Uncommon dementias (including the prion diseases)
ByMatthew Jones, David Neary
Pages 13

Relatively common conditions such as Alzheimer’s disease (AD), dementia with Lewy bodies (DLB) and cerebrovascular disease account for the majority of dementia cases seen in clinical practice. However, a large number of neurological and systemic disorders may also cause progressive cognitive and behavioural syndromes. Many of these disorders cause early-onset dementia and a signicant proportion is amenable to some form of treatment. us, the recognition of rare causes of dementia is an important skill for all those involved in the diagnosis and care of people with dementia syndromes.