ABSTRACT
INTRODUCTION Hydrocephalus in primary craniosynostosis, a condition that should not be confused with shunt-induced secondary synostosis (1), is unique in terms of pathogenesis, clinical appearance, and management. First reports about this disorder were published in the very early days of craniofacial surgery (2,3), but knowledge was scarce in former decades, as it was based on incidental findings or on small, highly selected series (4). Only the widespread use of computerized tomography (CT) and magnetic resonance imaging (MRI) permitted systematic studies addressing the questions of incidence, pathogenesis, and clinical significance of dilated ventricles in craniosynostosis (5-8). During the last decade, a number of studies substantially enhanced our knowledge, although many questions still remain (9-16).
