ABSTRACT

A variety of names exist for the pathological entity that was originally called pseudotumor cerebri over a century ago. It is a condition defined by the presence of pathologically raised intracranial pressure in the absence of dilated ventricles or intracranial mass lesion with normal CSF composition. The underlying mechanism of raised intracranial pressure without manifestations of a focal lesion or focal deficit remains incompletely understood. Therefore many different concepts for etiology, investigation, and management have evolved over the years. The ultimate treatment of this elusive condition overlaps among neurologist, ophthalmologist, and neurosurgeon.