ABSTRACT
Clinical features affecting the lungs include: • restriction of chest wall movement; • fusion of the costovertebral joints; • leads to increasing breathlessness; • increased number of respiratory infections including pneumonia; • apical fibrosis which may cavitate simulating tuberculosis; • aspergilloma within these cavities; • respiratory failure, particularly after upper abdominal surgery when
diaphragmatic movement may become difficult due to pain (chest wall movement greatly reduced).
