ABSTRACT

Gastrointestinal bleeding in Klippel-Trenaunay syndrome is a rare condition. The source of the bleeding is usually found in the descending colon and rectum, and it originates from ectatic venous vessels in the colon submucosa. There is a variety of possible treatments from conservative supportive treatments to surgical resection. The invasiveness of the procedures is based on the clinical symptomatology and the hemodynamic stability of a patient. We also have to be prepared to encounter the clotting problems of Klippel-Trenaunay syndrome, such as “consumptive coagulopathy and thromboembolic complications.”