ABSTRACT

Cystic fibrosis (CF) is a genetic disorder in which sufferers have a failure of pancreatic enzyme secretion and malabsorption. They are also susceptible to pulmonary infection. The majority of patients in the United Kingdom have chronic pulmonary infection with the organism Pseudomonas aeruginosa by their late teens. Much CF therapy is directed towards improving nutrition and preventing, or managing, chronic infection with P. aeruginosa.