ABSTRACT

Multiple endocrine neoplasia (MEN) syndromes are infrequently encountered syndromes predominantly involving endocrine glands that predispose the patient to develop benign and malignant neoplasms of various endocrine and non-endocrine organs. Described first in the early-twentieth century, their number continues to grow along with improvements in the understanding of these intriguing. The more common and better understood MEN syndromes have been described earlier. This chapter deals with disorders afflicting various endocrine glands that are not clubbed as MEN 1 and MEN 2, like Carney complex, hyperparathyroidism-jaw tumor (HPT-JT) syndrome, and neonatal HPT, which will be described here. These are rare entities, but their timely diagnosis and intervention help improve outcomes.