ABSTRACT
Primary lymphedema is caused by a congenital abnormality or dysfunction in the lymphatic system and can be further classified according to age of onset. Primary lymphedema is rare, affecting 1.15 per 100,000 people younger than 20 years of age. Alternatively, primary lymphedema can be classified according to the abnormality found in the lymphatics. Secondary lymphedema is edema due to a reduction in lymph flow by an acquired cause. The causes of secondary lymphedema include trauma, recurrent infection, and malignancy and its treatment. In the developed world, the most common cause of secondary lymphedema is malignancy (including that resulting from cancer treatment). This chapter will be emphasizing secondary lymphedema related to cancer and its treatment, which is frequently overlooked. The International Society of Lymphology Executive Committee in 2013 revised a consensus document that offered an integrated view of the management of lymphedema. The role of weight control and regular exercises in the management of lymphedema is thought to be important.
