ABSTRACT
The term lymphangioma circumscriptum includes congenital and acquired benign cystic dilatations involving the superficial lymphatic vessels. The incidence of both congenital and acquired forms of lymphangioma circumscriptum in the genital region is low. Lymphangioma circumscriptum may be caused by a congenital developmental anomaly of lymphatic vessels that leads to enlargement and sequestration of lymph fluid. Acquired lymphangiectasias of the genitalia result from damage and/or obstruction of previously normal lymphatic vessels of the pelvic area, usually developing as a result of malignancies, Crohn disease, surgery, radiotherapy, hidradenitis suppurativa and/or infections. Lymphangioma circumscriptum of the genital area may resemble different disorders, such as genital warts, molluscum contagiosum, herpes simplex, and angiokeratoma. Dermoscopy and reflectance confocal microscopy may be useful to confirm the clinical suspect and ultrasound for pre-operative evaluation of the margins. The term lymphangioma circumscriptum includes congenital and acquired benign cystic dilatations involving the superficial lymphatic vessels.
