ABSTRACT
Introduction: The Duane retraction syndrome (DRS)is an autosomal dominant hereditary disease, with a sporadical manifestation. The cause of pathological innervation of muscles of the bulbus is due to the congenital defect of intracranial centers. Instead of sixth cranial nerve, the lateral rec- tus muscles are innervated by the third cranial nerve. Main symptoms are: decreased abduction and adduction of the affected eye, narrowing of palpebral fissure and retraction of the bulbus oculi. There are three types by Huber according the clinical symptoms. We present a girl of 6 years suffering a bilateral form of DRS.
