ABSTRACT
Ebstein’s anomaly is a multi-faceted condition associated with a myriad of potential electrophysiological substrates. Despite the strong association with congenital accessory pathways, in practice, all forms of reentrant tachycardia are observed with increased frequency in this congenital heart lesion. Successful catheter ablation requires an in-depth knowledge of the embryology, anatomy, and electrophysiology that are unique to Ebstein’s anomaly. Moreover, the ramifications of surgical repair and their effect on the arrhythmia substrate should not be forgotten for this form of congenital heart disease. Optimal management requires close communication between the various members of the multispecialty teams that care for these patients.
