ABSTRACT

Interstitial lung diseases encompass a diverse group of more than 200 separate entities affecting the lung parenchyma. Because these conditions are multilobar and frequently bilateral in distribution on imaging, the term ‘diffuse parenchymal lung disease’ (DPLD) has been suggested as both more appropriate and less restrictive at the microscopic pathology level. Today the diagnosis of DPLD requires correlation of clinical, radiologic and histopathologic features for clinical relevance.