ABSTRACT
Wilms's tumour represents 6% to 7% of all paediatric malignancies and is the second most common intra-abdominal tumour in children. In North America the annual incidence in children is 8.1 per million and there are 650 newly diagnosed cases a year. The mean age at presentation is 3 years, and it is rare over 10 years and in those under 6 months of age. The risk of developing Wilms's tumour is more than 30%. Beckwith-Wiedemann's syndrome is an overgrowth disorder manifested by large birthweight, macroglossia, organomegaly, hemihypertrophy, neonatal hypoglycaemia, abdominal wall defects, ear abnormalities and a predisposition to the Wilms's tumour. A child with an abdominal mass requires the diagnostic imaging in order to establish the nature and origin of the mass. It is important to note that treatment protocols differ geographically.
