ABSTRACT

I. Preface ...................................................................................................................................252 A. Definition...................................................................................................................252 B. History.......................................................................................................................253

II. Pathogenesis ..........................................................................................................................254 A. Pathological Features ................................................................................................254 B. HLA and the Autoimmune Mechanism ...................................................................254 C. Hyperestrogenism......................................................................................................258

III. Clinical Manifestations .........................................................................................................258 A. Clinical Presentations................................................................................................260 B. Regional Differences.................................................................................................261

IV. Diagnosis ...............................................................................................................................262 A. Diagnostic Criteria ....................................................................................................262 B. Angiographic Classifications ....................................................................................263 C. Laboratory Tests and Imaging Modalities................................................................265