ABSTRACT
Neuroepithelial tumors of the eye are rare and typically occur in the ciliary body but can also involve the iris and retina. They may be congenital or acquired. Congenital tumors include medulloepitheliomas and glioneuromas, while acquired tumors include adenomas and adenocarcinomas. The congenital tumors typically involve the nonpigment ciliary epithelium (NPCE), whereas the acquired tumors involve the ciliary pigment epithelium (CPE), the NPCE, the retinal pigment epithelium (RPE), and the iris pigment epithelium (IPE).
