ABSTRACT

The definition of the Lennox-Gastaut syndrome remains controversial. It is most often defined as an epilepsy syndrome characterized by multiple seizure types, including brief tonic, atonic, myoclonic and atypical absence seizures, associated with an interictal EEG pattern of diffuse, slow (2.5 Hz) spike-wave complexes.1 Intellectual disability is a very frequent but not a constant feature.2 Episodes of nonconvulsive status epilepticus occur frequently. Some authors3,4 consider that two additional criteria are necessary for the diagnosis: the occurrence of generalized tonic seizures, and runs of fast (10 Hz) rhythms, which occur especially during non-REM sleep, with or without tonic seizures.