ABSTRACT
Introduction Epidemiology Natural history Pathologic characteristics Etiopathogenesis Clinical presentation Diagnosis Management Ablation outcome
INTRODUCTION Arrhythmogenic right ventricular dysplasia (ARVD) is a progressive, genetically determined heart muscle disease, that is characterized by structural and functional abnormalities involving mostly the right ventricle (RV) and at a later stage may affect the left ventricle as well.1 Pathologically there is RV myocardial atrophy, and fibrofatty replacement, which clinically leads to RV functional deterioration and electrical instability that may predispose to life-threatening ventricular arrhythmia, heart failure, and sudden death.2
