ABSTRACT
The dislocation of the entire lens with an intact lens capsule is a rare occurrence. It is encountered in certain ocular conditions, such as Marfan’s syndrome, homocystinuria, hyperlysinemia, EhlersDanlos syndrome, Weill-Marchesani syndrome, scleroderma, and trauma, etc. The lens subluxation is usually in an upward and temporal direction in Marfan’s syndrome and Weill-Marchesani syndrome, while it is often downward in homocystinuria.1 The intact dislocated lens rarely causes much intraocular inflammation, and the resulting refractive error can often be corrected with an aphakic contact lens without any surgical intervention. However, sometimes the ectopic lens may be associated with intraocular inflammation, glaucoma, retinal breaks, or a retinal detachment. Even in the absence of a sight-threatening intraocular problem, the movement of the ectopic lens with a change in body position may induce bothersome visual symptoms. In such a situation, the removal of the dislocated lens may be warranted.
