ABSTRACT
I. Introduction Throughout its history, cystic fibrosis (CF) has been identified in the public imagination as a fatal disease. Readers with even a passing familiarity with CF will recognize this as an outdated characterization: in the 21st century, CF is a manageable chronic illness, still with a limited life span, but with an increasingly healthy childhood population and an enlarging cohort of adults (1). Given the changing epidemiology of those living with CF, our goal in this chapter is twofold: first, to describe state-of-the-art palliative care throughout the lifespan of the child and adult with CF, and second, to describe highquality CF end-of-life care, which for the purposes of this chapter is defined as care for the family and patient during the last two months of life and bereavement care following the death of the patient.
