ABSTRACT
Sacrococcygeal teratomas are the most common fetal tumors with an incidence of about 1:40,000 births. These tumors are derived from multipotential embryonic cells, and most of them are external tumors with a variable pelvic component, arising at the level of sacrum at coccyx. They can be very large and are usually heterogenic with cystic and solid components. Polyhydramnios can develop secondary to the hyperdynamic circulation or in case of anemia secondary to intratumor bleeding. Most of the sacrococcygeal teratomas are benign with less than 10% showing a malignant component. Rapidly growing tumors, tumors with large intraperitoneal component, and the development of polyhydramnios or hydrops are associated with the worst prognosis.
