ABSTRACT

Hypertrophic obstructive cardiomyopathy, also known as idiopathic hyper­ trophic subaortic stenosis (IHSS), is a autosomal dominant disease in which there is hypertrophy of the interventricular septum classically in the cephalad portion, hence the term asymmetric septal hypertrophy. Systolic anterior motion of the anterior leaflet of the mitral valve occurs due to the free edge of the anterior leaflet bulging close to the septum, causing an abnormal motion seen on echo­ cardiography. An echocardiogram is the most helpful diagnostic maneuver in evalu­ ating IHSS. If the patient is refractory to medical treatment (Inderal, calcium chan­ nel blockers and diuretics), then the patient should undergo cardiac catheteriza­ tion with a view to surgery.