ABSTRACT

The Sturge-Weber syndrome, also known as the Sturge-Weber-Dimitri syndrome or encephalotrigeminal angiomatosis, first described by William Sturge in 1879 (Sturge 1879), is a rare disorder, characterized, classically, by a unilateral facial port-wine stain, epilepsy, hemiplegia, and mental retardation, and, on appropriate imaging, cerebral cortical calcification in the hemisphere ipsilateral to the port-wine stain (Chao 1959; Lichtenstein 1954; PascualCastroviejo et al. 1993; Petermann et al. 1958; Sujansky and Conradi 1995a,b).