ABSTRACT
Congenital airway malformations include a wide spectrum of
pathology that occurs at various anatomic levels. Presenta-
tion varies widely, and is influenced both by the level at which
obstruction occurs and the severity of obstruction. In view of
the distinct anatomy of the pediatric airway and the
possibility of airway symptoms quickly progressing to life-
threatening airway compromise, early detection, diagnosis,
and treatment are imperative. The aim of this chapter is to
briefly discuss anomalies extending from larynx to the distal
airway, highlighting symptomatology, patient assessment,
and primary management strategies.