ABSTRACT

Congenital duodenal obstruction is the most common cause

of intestinal obstruction in the newborn period, occurring in

1 in 500010000 live births.13

Duodenal obstruction is the result of intrinsic lesion,

extrinsic lesion, or a combination of both. Intrinsic duodenal

obstruction may be caused by duodenal atresia, stenosis,

diaphragm, a perforated diaphragm, or a ‘windsock’ web.

The windsock web is a duodenal membrane which is

ballooned distally as a result of peristalsis from above.4,5

Extrinsic duodenal obstruction may be caused by annular

pancreas, malrotation, or preduodenal portal vein. Although

the annular pancreas forms a constricting ring around the

second part of the duodenum (Fig. 49.1), it is not believed to

be the cause of duodenal obstruction6,7 and there is usually

an associated atresia or stenosis in patients with an annular

pancreas.810 Similarly, preduodenal portal vein has also

seldom been reported to be the cause of duodenal obstruc-

tion and it is often associated with other causes of intestinal

obstruction, such as malrotation or duodenal atresia.11,12